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Papillary Renal Cell Carcinoma (CUI C1306837) Suggest changes to this concept
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Terms & Properties

Concept Unique Identifier (CUI): C1306837

NCI Thesaurus Code: C6975  (see NCI Thesaurus info)

Semantic Type: Neoplastic Process

NCIt Definition: Also known as chromophil carcinoma, it represents a minority of renal cell carcinomas. It can be hereditary or sporadic. The sporadic papillary renal cell carcinoma is characterized by trisomy of chromosomes 7, 16, and 17, and loss of chromosome Y. The peak incidence is in the sixth and seven decades. It is classified as type 1 or 2, based on the cytoplasmic volume and the thickness of the lining neoplastic cells. The prognosis is more favorable than for conventional (clear cell) renal cell carcinoma. -- 2003

PDQ Definition: Also known as chromophil carcinoma, it represents a minority of renal cell carcinomas. It can be hereditary or sporadic. The sporadic papillary renal cell carcinoma is characterized by trisomy of chromosomes 7, 16, and 17, and loss of chromosome Y. The peak incidence is in the sixth and seven decades. It is classified as type 1 or 2, based on the cytoplasmic volume and the thickness of the lining neoplastic cells. The prognosis is more favorable than for conventional (clear cell) renal cell carcinoma. -- 2003 Check for active clinical trials using this agent. (NCI Thesaurus)

HPO Definition: The presence of renal cell carcinoma in the renal papilla. [HPO:probinson]

SNOMEDCT_US Definition: A rare subtype of renal cell carcinoma arising from the renal tubular epithelium and showing a papillary growth pattern, which typically manifests with haematuria, flank pain, palpable abdominal mass or nonspecific symptoms, such as fatigue, weight loss or fever. Symptoms related to metastatic spread, such as bone pain or persistent cough, are frequently associated since early diagnosis is not common. It is typically multifocal, bilateral, and in most cases sporadic, although different hereditary syndromes may predispose to the development of papillary renal cell carcinoma.

SNOMEDCT_US Definition: A rare subtype of renal cell carcinoma arising from the renal tubular epithelium and showing a papillary growth pattern, which typically manifests with hematuria, flank pain, palpable abdominal mass or nonspecific symptoms, such as fatigue, weight loss or fever. Symptoms related to metastatic spread, such as bone pain or persistent cough, are frequently associated since early diagnosis is not common. It is typically multifocal, bilateral, and in most cases sporadic, although different hereditary syndromes may predispose to the development of papillary renal cell carcinoma.

CTEP Definition: CTEP_For_FDA: 10033702/Papillary tumour of renal pelvis

Synonyms & Abbreviations: (see Synonym Details)
Chromophil Carcinoma of Kidney
Chromophil Carcinoma of the Kidney
Chromophil RCC
Chromophil renal cell carcinoma
Papillary (Chromophil) Renal Cell Carcinoma
Papillary renal carcinoma, malignant - (subtype)
Papillary Renal Cell Cancer
Papillary renal cell carcinoma (disorder)
Papillary renal cell carcinoma (morphologic abnormality)
Papillary renal cell carcinoma
RCCP
Renal Cell Carcinoma, Papillary

External Source Codes: 
NCI Thesaurus Code C6975 (see NCI Thesaurus info)

Other Properties: Property Definitions
Name Value Source
ACTIVE 1 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000448009 SNOMEDCT_US
CHARACTERISTIC_TYPE_ID 900000000000011006 SNOMEDCT_US
CODE_REF (C64.9) ICDO
Contributing_Source CTEP NCI
Contributing_Source CTRP NCI
CTV3ID XUxkp SNOMEDCT_US
CTV3ID XUxks SNOMEDCT_US
DATE_CREATED 2013-01-09T00:04:00 GARD
DATE_FIRST_PUBLISHED 2007-05-01 PDQ
DATE_LAST_MODIFIED 2012-03-28 PDQ
DATE_LAST_MODIFIED 2013-01-09T00:04:00 GARD
DEFINITION_STATUS_ID 900000000000073002 SNOMEDCT_US
DEFINITION_STATUS_ID 900000000000074008 SNOMEDCT_US
DISEASE_IDENTIFIER_ID 20308 GARD
DISEASE_IDENTIFIER_ID 20314 GARD
DISEASE_IDENTIFIER_ID 2459 GARD
EFFECTIVE_TIME 20170731 SNOMEDCT_US
HAS_GARD_PAGE true GARD
ICD-O-3_CODE 8260/3 SNOMEDCT_US
IDENTIFIER_TYPE_ID 1 GARD
IS_ACTIVE true GARD
IS_RARE true GARD
IS_SPANISH false GARD
LAST_REVIEW_DATE 2006-03-27T00:00:00 GARD
MODIFIER_ID 900000000000451002 SNOMEDCT_US
NCI_THESAURUS_CODE C6975 PDQ
Neoplastic_Status Malignant NCI
ORIG_STY Neoplasm diagnosis PDQ
PRIMARY_PATH 10078493$10068208$10038364$10029104$Papillary renal cell carcinoma$Renal neoplasms malignant$Renal and urinary tract neoplasms malignant and unspecified$Neoplasms benign, malignant and unspecified (incl cysts and polyps) MDR
PRIMARY_SOC 10029104 MDR
PT_IN_VERSION 19.1 MDR
PT_IN_VERSION 20.0 MDR
PT_IN_VERSION 20.1 MDR
RARE_DISEASE_URL http://rarediseases.info.nih.gov/gard/9572/papillary-renal-cell-carcinoma/resources/1 GARD
RARE_DISEASE_URL http://rarediseases.info.nih.gov/gard/9575/chromophil-renal-cell-carcinoma/resources/1 GARD
SID HP:0006776 HPO
SMQ_TERM_ADDVERSION 19.1 MDR
SMQ_TERM_CAT A MDR
SMQ_TERM_LEVEL 4 MDR
SMQ_TERM_LMVERSION 20.0 MDR
SMQ_TERM_SCOPE 2 MDR
SMQ_TERM_STATUS A MDR
SMQ_TERM_WEIGHT 0 MDR
SUBSET_MEMBER 446608001~MAPTARGET~8260/3 SNOMEDCT_US
SUBSET_MEMBER 447562003~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPADVICE~ALWAYS C64 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPTARGET~C64 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~ALWAYS C64.9 | CONSIDER LATERALITY SPECIFICATION SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~C64.9 SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~XUxkp SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~XUxks SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
TERM_LEVEL Related ICDO
TERMUI T637042 MSH
TERMUI T782077 MSH
TERMUI T811435 MSH
TH NLM (2006) MSH
TH NLM (2012) MSH
TH OMIM (2013) MSH
TH ORD (2010) MSH
TYPE_ID 900000000000003001 SNOMEDCT_US
TYPE_ID 900000000000013009 SNOMEDCT_US

Additional Concept Data:  (none)

URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C1306837

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