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Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor (CUI C0684337) Suggest changes to this concept
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Terms & Properties

Concept Unique Identifier (CUI): C0684337

NCI Thesaurus Code: C27291  (see NCI Thesaurus info)

Semantic Type: Neoplastic Process

NCIt Definition: A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms.

CTEP Definition: CTEP_For_FDA: 10015563/Ewing's sarcoma NOS

HPO Definition: A primitive neuroectodermal neoplasm that occurs extracranially in soft tissue and bone. []

NCI-GLOSS Definition: A group of cancers that includes Ewing tumor of bone (ETB or Ewing sarcoma of bone), extraosseous Ewing (EOE) tumors, primitive neuroectodermal tumors (PNET or peripheral neuroepithelioma), and Askin tumors (PNET of the chest wall). These tumors all come from the same type of stem cell.

Synonyms & Abbreviations: (see Synonym Details)
(pPNET) Peripheral Primitive Neuroectodermal Tumors
Askin’s tumor (PNET of the chest wall) (type)
EFTs
Ewing family of tumors
Ewing sarcoma / peripheral neuroectodermal tumor (morphologic abnormality)
Ewing sarcoma / peripheral neuroectodermal tumor
Ewing sarcoma / peripheral neuroectodermal tumour
Ewing sarcoma / PNET
Ewing sarcoma family of tumors
Ewing sarcoma/Peripheral PNET
Ewing sarcoma/peripheral primitive neuroectodermal tumor (PNET)
Ewing sarcoma/Peripheral primitive neuroectodermal tumor
Ewing sarcoma/PNET
Ewing sarcoma/primitive neuroectodermal tumor (PNET)
Ewing tumor/peripheral primitive neuroectodermal tumor
Ewing's family of tumors
Ewing's Family of Tumours
Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor
Ewing's sarcoma/primitive neuroectodermal tumor (PNET)
Ewings sarcoma-primitive neuroectodermal tumor (PNET)
Ewing’s tumor of bone (type)
Extracranial Primitive Neuroectodermal Tumor
Extraosseous Ewing’s (tumor growing outside of the bone) (type)
Neuroectodermal Neoplasm, Peripheral Primitive
Neuroectodermal Tumor, Peripheral Primitive
Neuroectodermal Tumor, Peripheral
Neuroepithelioma, Peripheral
Neuroepitheliomas, Peripheral
Peripheral Neuroepitheliomas
Peripheral Neuroepithelioma
Peripheral primitive neuroectodermal neoplasm
Peripheral Primitive Neuroectodermal Tumors
PNET
Primitive neuroectodermal tumor (PNET) (type)
primitive neuroectodermal tumor (PNET)
Primitive Neuroectodermal Tumor, Extracranial
Tumors of Ewing's Family
Tumors of the Ewing's Family

External Source Codes: 
NCI Thesaurus Code C27291 (see NCI Thesaurus info)

Other Properties: Property Definitions
Name Value Source
ACTIVE 1 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000017005 SNOMEDCT_US
Contributing_Source CTEP NCI
Contributing_Source CTRP NCI
CTV3ID XUnKQ SNOMEDCT_US
DATE_CREATED 2013-01-09T00:04:00 GARD
DATE_LAST_MODIFIED 2007-05-03 PDQ
DATE_LAST_MODIFIED 2013-01-09T00:04:00 GARD
DEFINITION_STATUS_ID 900000000000074008 SNOMEDCT_US
DISEASE_IDENTIFIER_ID 19927 GARD
DISEASE_IDENTIFIER_ID 19928 GARD
DISEASE_IDENTIFIER_ID 19929 GARD
DISEASE_IDENTIFIER_ID 19930 GARD
DISEASE_IDENTIFIER_ID 19931 GARD
EFFECTIVE_TIME 20140731 SNOMEDCT_US
HAS_GARD_PAGE true GARD
IDENTIFIER_TYPE_ID 1 GARD
IS_ACTIVE true GARD
IS_RARE true GARD
IS_SPANISH false GARD
LAST_REVIEW_DATE 2007-06-27T00:00:00 GARD
Neoplastic_Status Malignant NCI
ORIG_STY Neoplasm diagnosis PDQ
PID 21 PDQ
RARE_DISEASE_URL http://rarediseases.info.nih.gov/gard/9323/ewings-family-of-tumors/resources/1 GARD
SUBSET_MEMBER 900000000000497000~MAPTARGET~XUnKQ SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
TERMUI T054520 MSH
TERMUI T372801 MSH
TERMUI T372802 MSH
TERMUI T372803 MSH
TERMUI T372804 MSH
TERMUI T372805 MSH
TERMUI T372807 MSH
TERMUI T372808 MSH
TERMUI T812400 MSH
TH NLM (1994) MSH
TH NLM (2000) MSH
TH OMIM (2013) MSH
TYPE_ID 900000000000003001 SNOMEDCT_US
TYPE_ID 900000000000013009 SNOMEDCT_US

Additional Concept Data:  (none)

URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0684337

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