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| Terms & Properties |
Concept Unique Identifier (CUI): C0684337
NCI Thesaurus Code: C27291 (see NCI Thesaurus info)
Semantic Type: Neoplastic Process
NCIt Definition: A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms.
CTEP Definition: CTEP_For_FDA: 10015563/Ewing's sarcoma NOS
HPO Definition: A primitive neuroectodermal neoplasm that occurs extracranially in soft tissue and bone. []
NCI-GLOSS Definition: A group of cancers that includes Ewing tumor of bone (ETB or Ewing sarcoma of bone), extraosseous Ewing (EOE) tumors, primitive neuroectodermal tumors (PNET or peripheral neuroepithelioma), and Askin tumors (PNET of the chest wall). These tumors all come from the same type of stem cell.
Synonyms & Abbreviations: (see Synonym Details)
| (pPNET) Peripheral Primitive Neuroectodermal Tumors |
| Askin’s tumor (PNET of the chest wall) (type) |
| EFTs |
| Ewing family of tumors |
| Ewing sarcoma / peripheral neuroectodermal tumor (morphologic abnormality) |
| Ewing sarcoma / peripheral neuroectodermal tumor |
| Ewing sarcoma / peripheral neuroectodermal tumour |
| Ewing sarcoma / PNET |
| Ewing sarcoma family of tumors |
| Ewing sarcoma/Peripheral PNET |
| Ewing sarcoma/peripheral primitive neuroectodermal tumor (PNET) |
| Ewing sarcoma/Peripheral primitive neuroectodermal tumor |
| Ewing sarcoma/PNET |
| Ewing sarcoma/primitive neuroectodermal tumor (PNET) |
| Ewing tumor/peripheral primitive neuroectodermal tumor |
| Ewing's family of tumors |
| Ewing's Family of Tumours |
| Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor |
| Ewing's sarcoma/primitive neuroectodermal tumor (PNET) |
| Ewings sarcoma-primitive neuroectodermal tumor (PNET) |
| Ewing’s tumor of bone (type) |
| Extracranial Primitive Neuroectodermal Tumor |
| Extraosseous Ewing’s (tumor growing outside of the bone) (type) |
| Neuroectodermal Neoplasm, Peripheral Primitive |
| Neuroectodermal Tumor, Peripheral Primitive |
| Neuroectodermal Tumor, Peripheral |
| Neuroepithelioma, Peripheral |
| Neuroepitheliomas, Peripheral |
| Peripheral Neuroepitheliomas |
| Peripheral Neuroepithelioma |
| Peripheral primitive neuroectodermal neoplasm |
| Peripheral Primitive Neuroectodermal Tumors |
| PNET |
| Primitive neuroectodermal tumor (PNET) (type) |
| primitive neuroectodermal tumor (PNET) |
| Primitive Neuroectodermal Tumor, Extracranial |
| Tumors of Ewing's Family |
| Tumors of the Ewing's Family |
External Source Codes:
| NCI Thesaurus Code | C27291 (see NCI Thesaurus info) |
Other Properties:
| Name | Value | Source |
|---|---|---|
| ACTIVE | 1 | SNOMEDCT_US |
| CASE_SIGNIFICANCE_ID | 900000000000017005 | SNOMEDCT_US |
| Contributing_Source | CTEP | NCI |
| Contributing_Source | CTRP | NCI |
| CTV3ID | XUnKQ | SNOMEDCT_US |
| DATE_CREATED | 2013-01-09T00:04:00 | GARD |
| DATE_LAST_MODIFIED | 2007-05-03 | PDQ |
| DATE_LAST_MODIFIED | 2013-01-09T00:04:00 | GARD |
| DEFINITION_STATUS_ID | 900000000000074008 | SNOMEDCT_US |
| DISEASE_IDENTIFIER_ID | 19927 | GARD |
| DISEASE_IDENTIFIER_ID | 19928 | GARD |
| DISEASE_IDENTIFIER_ID | 19929 | GARD |
| DISEASE_IDENTIFIER_ID | 19930 | GARD |
| DISEASE_IDENTIFIER_ID | 19931 | GARD |
| EFFECTIVE_TIME | 20140731 | SNOMEDCT_US |
| HAS_GARD_PAGE | true | GARD |
| IDENTIFIER_TYPE_ID | 1 | GARD |
| IS_ACTIVE | true | GARD |
| IS_RARE | true | GARD |
| IS_SPANISH | false | GARD |
| LAST_REVIEW_DATE | 2007-06-27T00:00:00 | GARD |
| Neoplastic_Status | Malignant | NCI |
| ORIG_STY | Neoplasm diagnosis | PDQ |
| PID | 21 | PDQ |
| RARE_DISEASE_URL | http://rarediseases.info.nih.gov/gard/9323/ewings-family-of-tumors/resources/1 | GARD |
| SUBSET_MEMBER | 900000000000497000~MAPTARGET~XUnKQ | SNOMEDCT_US |
| SUBSET_MEMBER | 900000000000508004~ACCEPTABILITYID~900000000000548007 | SNOMEDCT_US |
| SUBSET_MEMBER | 900000000000508004~ACCEPTABILITYID~900000000000549004 | SNOMEDCT_US |
| SUBSET_MEMBER | 900000000000509007~ACCEPTABILITYID~900000000000548007 | SNOMEDCT_US |
| SUBSET_MEMBER | 900000000000509007~ACCEPTABILITYID~900000000000549004 | SNOMEDCT_US |
| TERMUI | T054520 | MSH |
| TERMUI | T372801 | MSH |
| TERMUI | T372802 | MSH |
| TERMUI | T372803 | MSH |
| TERMUI | T372804 | MSH |
| TERMUI | T372805 | MSH |
| TERMUI | T372807 | MSH |
| TERMUI | T372808 | MSH |
| TERMUI | T812400 | MSH |
| TH | NLM (1994) | MSH |
| TH | NLM (2000) | MSH |
| TH | OMIM (2013) | MSH |
| TYPE_ID | 900000000000003001 | SNOMEDCT_US |
| TYPE_ID | 900000000000013009 | SNOMEDCT_US |
Additional Concept Data: (none)
URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0684337
