skip navigation links
National Cancer Institute
Enterprise Vocabulary Services
Box
NCIm Version: 201808 (Browser Version 2.9, using LexEVS 6.5.1)
SearchBox Top
SearchBox Bottom
Lung Diseases, Interstitial (CUI C0206062) Suggest changes to this concept
Add to Cart

Terms & Properties

Concept Unique Identifier (CUI): C0206062

Semantic Type: Disease or Syndrome

HPO Definition: Abnormality of the lung parenchyma extending to the pulmonary interstitium and leading to diffuse pulmonary fibrosis. [HPO:probinson]

MEDLINEPLUS Definition: 

Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. The inflammation and scarring make it hard to get enough oxygen. The scarring is called pulmonary fibrosis.

Breathing in dust or other particles in the air is responsible for some types of interstitial lung diseases. Specific types include

  • Black lung disease among coal miners, from inhaling coal dust
  • Farmer's lung, from inhaling farm dust
  • Asbestosis, from inhaling asbestos fibers
  • Siderosis, from inhaling iron from mines or welding fumes
  • Silicosis, from inhaling silica dust

Other causes include autoimmune diseases or occupational exposures to molds, gases, or fumes. Some types of interstitial lung disease have no known cause.

Treatment depends on the type of exposure and the stage of the disease. It may involve medicines, oxygen therapy, or a lung transplant in severe cases.

CSP Definition: heterogeneous group of noninfectious, nonmalignant disorders of the lower respiratory tract, affecting primarily the alveolar wall structures but also often involving the small airways and blood vessels of the lung parenchyma; may lead to respiratory insufficiency and death.

MSH Definition: A diverse group of lung diseases that affect the lung parenchyma. They are characterized by an initial inflammation of PULMONARY ALVEOLI that extends to the interstitium and beyond leading to diffuse PULMONARY FIBROSIS. Interstitial lung diseases are classified by their etiology (known or unknown causes), and radiological-pathological features.

Synonyms & Abbreviations: (see Synonym Details)
Diffuse Parenchymal Lung Diseases
Diffuse parenchymal lung disease
ILD - Interstitial lung disease
ILD
interstitial disease
Interstitial lung disease (disorder)
Interstitial Lung Diseases
INTERSTITIAL LUNG DISEASE
INTERSTITIAL LUNG DIS
Interstitial pulmonary disease, unspecified
Interstitial pulmonary disease
LUNG DIS INTERSTITIAL
Lung Disease, Interstitial
Lung Diseases, Interstitial [Disease/Finding]
Lung Diseases, Interstitial

External Source Codes:  (none)

Other Properties: Property Definitions
Name Value Source
ACTIVE 1 SNOMEDCT_US
AN general or unspecified; prefer specifics; DF: LUNG DIS INTERSTITIAL MSH
AQL BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI MSH
CASE_SIGNIFICANCE_ID 900000000000017005 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000448009 SNOMEDCT_US
CITE Playbook RADLEX
COMMENT 'interstitial' ' exists as its own class, so not included as a synonym here. RADLEX
CTV3ID X102V SNOMEDCT_US
DATE_CREATED 08/24/2010 MEDLINEPLUS
DC 1 MSH
DEFINITION_STATUS_ID 900000000000073002 SNOMEDCT_US
DID 4007-0072 CSP
DX 19940101 MSH
EFFECTIVE_TIME 20040731 SNOMEDCT_US
HN 94; was LUNG DISEASE, INTERSTITIAL see PULMONARY FIBROSIS 1985-93; PNEUMONITIS, INTERSTITIAL was see PULMONARY FIBROSIS 1985-93; PNEUMONIA, INTERSTITIAL was see under PULMONARY FIBROSIS 1963-74, was see PULMONARY FIBROSIS 1975-93 MSH
IAN DEFAULT ICD10
INCLUSION_TERM Interstitial pneumonia NOS ICD10
MDA 19930603 MSH
MESH_DEFINITION A diverse group of lung diseases that affect the lung parenchyma. They are characterized by an initial inflammation of PULMONARY ALVEOLI that extends to the interstitium and beyond leading to diffuse PULMONARY FIBROSIS. Interstitial lung diseases are classified by their etiology (known or unknown causes), and radiological-pathological features. NDFRT
MESH_DUI D017563 NDFRT
MESH_NAME Lung Diseases, Interstitial NDFRT
MESH_UI M0026626 NDFRT
MMR 20080708 MSH
MN C08.381.483 MSH
MP_HEALTH_TOPIC_URL https://www.nlm.nih.gov/medlineplus/interstitiallungdiseases.html MEDLINEPLUS
MP_OTHER_LANGUAGE_URL Spanish https://www.nlm.nih.gov/medlineplus/spanish/interstitiallungdiseases.html MEDLINEPLUS
MP_PRIMARY_INSTITUTE_URL National Heart, Lung, and Blood Institute http://www.nhlbi.nih.gov/ MEDLINEPLUS
NDFRT_KIND DISEASE_KIND NDFRT
NUI N0000003603 NDFRT
OL use PULMONARY FIBROSIS to search LUNG DISEASE, INTERSTITIAL & PNEUMONITIS, INTERSTITIAL 1985-93 & PNEUMONIA, INTERSTITIAL 1966-93 MSH
ORDER_NO 12697 ICD10CM
PM 94; was LUNG DISEASE, INTERSTITIAL see PULMONARY FIBROSIS 1985-93; PNEUMONITIS, INTERSTITIAL was see PULMONARY FIBROSIS 1985-93; PNEUMONIA, INTERSTITIAL was see under PULMONARY FIBROSIS 1963-74, was see PULMONARY FIBROSIS 1975-93 MSH
PRIMARY_PATH 10022611$10033979$10024967$10038738$Interstitial lung disease$Parenchymal lung disorders NEC$Lower respiratory tract disorders (excl obstruction and infection)$Respiratory, thoracic and mediastinal disorders MDR
PRIMARY_SOC 10038738 MDR
PT_IN_VERSION 10.0 MDR
PT_IN_VERSION 10.1 MDR
PT_IN_VERSION 11.0 MDR
PT_IN_VERSION 11.1 MDR
PT_IN_VERSION 12.0 MDR
PT_IN_VERSION 12.1 MDR
PT_IN_VERSION 13.0 MDR
PT_IN_VERSION 13.1 MDR
PT_IN_VERSION 14.0 MDR
PT_IN_VERSION 14.1 MDR
PT_IN_VERSION 15.0 MDR
PT_IN_VERSION 15.1 MDR
PT_IN_VERSION 16.0 MDR
PT_IN_VERSION 16.1 MDR
PT_IN_VERSION 17.0 MDR
PT_IN_VERSION 17.1 MDR
PT_IN_VERSION 18.0 MDR
PT_IN_VERSION 18.1 MDR
PT_IN_VERSION 19.0 MDR
PT_IN_VERSION 19.1 MDR
PT_IN_VERSION 20.0 MDR
PT_IN_VERSION 20.1 MDR
PT_IN_VERSION 8.0 MDR
PT_IN_VERSION 8.1 MDR
PT_IN_VERSION 9.0 MDR
PT_IN_VERSION 9.1 MDR
RXAUI 3182434 RXNORM
RXAUI 3190279 RXNORM
RXAUI 3190280 RXNORM
RXAUI 3287117 RXNORM
RXCUI 1028101 RXNORM
SID HP:0006513 HPO
SID HP:0006547 HPO
SMQ_TERM_ADDVERSION 12.0 MDR
SMQ_TERM_ADDVERSION 16.0 MDR
SMQ_TERM_ADDVERSION 19.0 MDR
SMQ_TERM_ADDVERSION 9.0 MDR
SMQ_TERM_CAT A MDR
SMQ_TERM_CAT B MDR
SMQ_TERM_CAT C MDR
SMQ_TERM_LEVEL 4 MDR
SMQ_TERM_LMVERSION 12.0 MDR
SMQ_TERM_LMVERSION 16.0 MDR
SMQ_TERM_LMVERSION 19.0 MDR
SMQ_TERM_LMVERSION 9.0 MDR
SMQ_TERM_SCOPE 1 MDR
SMQ_TERM_SCOPE 2 MDR
SMQ_TERM_STATUS A MDR
SMQ_TERM_WEIGHT 0 MDR
SNOMED_CID 233703007 NDFRT
SUBSET_MEMBER 447562003~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPADVICE~ALWAYS J84.9 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPTARGET~J84.9 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~ALWAYS J84.9 | DESCENDANTS NOT EXHAUSTIVELY MAPPED SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~IF AGE AT ONSET OF CLINICAL FINDING BEFORE 18.0 YEARS CHOOSE J84.848 | DESCENDANTS NOT EXHAUSTIVELY MAPPED | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447639009 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~2 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~IFA 445518008 | Age at onset of clinical finding (observable entity) | < 18.0 years SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~OTHERWISE TRUE SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~J84.848 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~J84.9 SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~X102V SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
TERMUI T052665 MSH
TERMUI T052666 MSH
TERMUI T703021 MSH
TH NLM (1994) MSH
TH NLM (2009) MSH
TYPE_ID 900000000000003001 SNOMEDCT_US
TYPE_ID 900000000000013009 SNOMEDCT_US

Additional Concept Data:  (none)

URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0206062

Mainbox Bottom