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Takayasu Arteritis (CUI C0039263) Suggest changes to this concept
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Terms & Properties

Concept Unique Identifier (CUI): C0039263

NCI Thesaurus Code: C35062  (see NCI Thesaurus info)

Semantic Type: Disease or Syndrome

NCIt Definition: A large vessel vasculitis affecting the aorta and its branches. It usually affects young females. It causes vascular obstruction, resulting in asymmetric pulses.

RADLEX Definition: A thrombo-obliterative process of the great vessels stemming from the aortic arch, occurring generally in young women. Radial and carotid pulses are typically obliterated. Skin changes are due to the disturbed circulation. There may be loss of hair and atrophy of the skin and its appendages with underlying muscle atrophy. (Andrews' Diseases of the Skin, 8th ed) [MeSH]

GARD Definition: Takayasu arteritis is a condition that causes inflammation of the main blood vessel that carries blood from the heart to the rest of the body (aorta) and its associated branched blood vessels. As a result of the inflammation, the blood vessel walls become thick and make it difficult for blood to flow. Over time, impaired blood flow causes damage to the heart and various other organs of the body.  Although the cause remains unknown, Takayasu arteritis appears to be an autoimmune condition, in which cells that fight infection and disease are wrongly targeted against the body's own tissues. - this information is from GARD/ORDR/NCATS.

NICHD Definition: A large vessel granulomatous vasculitis affecting the aorta or its main branches and pulmonary arteries with angiographic findings of stenosis, occlusion, or aneurysm. Clinical findings include absent or asymmetric pulses (discrepancy in four limb blood pressure), bruits, hypertension, or elevation in acute phase reactants.

MSH Definition: A chronic inflammatory process that affects the AORTA and its primary branches, such as the brachiocephalic artery (BRACHIOCEPHALIC TRUNK) and CAROTID ARTERIES. It results in progressive arterial stenosis, occlusion, and aneurysm formation. The pulse in the arm is hard to detect. Patients with aortitis syndrome often exhibit retinopathy.

Synonyms & Abbreviations: (see Synonym Details)
Acquired aortoarteritis
Aortic arch arteritis
Aortic arch syndrome [Takayasu]
Aortic arch syndrome
Arteritides, Young Female
Arteritis, Takayasu's
Arteritis, Takayasus
ARTERITIS, TAKAYASU
Arteritis, Young Female
Atypical coarctation
BRACHIOCEPHALIC ISCHEMIA
Disease, Takayasu
Female Arteritides, Young
Female Arteritis, Young
Idiopathic aortitis (disorder)
Idiopathic aortitis
Idiopathic medial aortopathy AND arteriopathy
MARTORELL SYNDROME
Nonspecific aortoarteritis
Nonspecific arteritis
Occlusive thromboarteriopathy
Primary arteritis
Pulseless Disease
PULSELESS DIS
Raeder-Harbitz syndrome
Reverse coarctation
Sclerosing aortitis AND arteritis
TAKAYASU ARTERIOPATHY
Takayasu Arteritis [Disease/Finding]
Takayasu arteritis
TAKAYASU DISEASE
Takayasu Syndrome
Takayasu's arteriopathy
Takayasu's arteritis
Takayasu's disease (disorder)
Takayasu's Disease
Takayasus Arteritis
TA
Young Female Arteritides
Young female arteritis

External Source Codes: 
NCI Thesaurus Code C35062 (see NCI Thesaurus info)

Other Properties: Property Definitions
Name Value Source
ACTIVE 1 SNOMEDCT_US
AQL BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI MSH
CASE_SIGNIFICANCE_ID 900000000000017005 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000020002 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000448009 SNOMEDCT_US
CHARACTERISTIC_TYPE_ID 900000000000011006 SNOMEDCT_US
Contributing_Source NICHD NCI
CTV3ID X705k SNOMEDCT_US
CTV3ID XE2QH SNOMEDCT_US
DATE_CREATED 2013-01-09T00:04:00 GARD
DATE_LAST_MODIFIED 2013-01-09T00:04:00 GARD
DC 1 MSH
DEFINITION_STATUS_ID 900000000000074008 SNOMEDCT_US
DISEASE_IDENTIFIER_ID 5944 GARD
DISEASE_IDENTIFIER_ID 5945 GARD
DISEASE_IDENTIFIER_ID 5946 GARD
DISEASE_IDENTIFIER_ID 5947 GARD
DISEASE_IDENTIFIER_ID 5948 GARD
DX 19910101 MSH
EFFECTIVE_TIME 20020131 SNOMEDCT_US
HAS_GARD_PAGE true GARD
HN 2008 (1963) MSH
IAN DEFAULT ICD10
ICE Aortic arch arteritis; Pulseless disease ICD9CM
IDENTIFIER_TYPE_ID 1 GARD
IS_ACTIVE true GARD
IS_RARE true GARD
IS_SPANISH false GARD
LAST_REVIEW_DATE 2009-12-15T00:00:00 GARD
MDA 19990101 MSH
MESH_DEFINITION A chronic inflammatory process that affects the AORTA and its primary branches, such as the brachiocephalic artery (BRACHIOCEPHALIC TRUNK) and CAROTID ARTERIES. It results in progressive arterial stenosis, occlusion, and aneurysm formation. The pulse in the arm is hard to detect. Patients with aortitis syndrome often exhibit retinopathy. NDFRT
MESH_DUI D013625 NDFRT
MESH_NAME Takayasu Arteritis NDFRT
MESH_UI M0021017 NDFRT
MIMTYPE 0 OMIM
MIMTYPEMEANING Other, mainly phenotypes with suspected mendelian basis OMIM
MIMTYPEVALUE none OMIM
MMR 20150623 MSH
MN C14.907.109.239.650 MSH
MN C14.907.940.090.800 MSH
MN C17.800.862.875 MSH
MODIFIER_ID 900000000000451002 SNOMEDCT_US
NDFRT_KIND DISEASE_KIND NDFRT
NICHD_Hierarchy_Term Takayasu Arteritis NCI
NUI N0000002897 NDFRT
ORDER_NO 17938 ICD10CM
PM 2008; see TAKAYASU'S ARTERITIS 1995-2007,see PULSELESS DISEASE 1993-1994, see TAKAYASU SYNDROME 1991-1992, see AORTIC ARCH SYNDROMES 1965-1990, see AORTIC DISEASES 1963-1964; for AORTITIS SYNDROME see AORTIC ARCH SYNDROMES 1987-2007 MSH
PRIMARY_PATH 10043097$10003231$10047116$10047065$Takayasu's arteritis$Arterial inflammations$Vascular inflammations$Vascular disorders MDR
PRIMARY_SOC 10047065 MDR
PT_IN_VERSION 10.0 MDR
PT_IN_VERSION 10.1 MDR
PT_IN_VERSION 11.0 MDR
PT_IN_VERSION 11.1 MDR
PT_IN_VERSION 12.0 MDR
PT_IN_VERSION 12.1 MDR
PT_IN_VERSION 13.0 MDR
PT_IN_VERSION 13.1 MDR
PT_IN_VERSION 14.0 MDR
PT_IN_VERSION 14.1 MDR
PT_IN_VERSION 15.0 MDR
PT_IN_VERSION 15.1 MDR
PT_IN_VERSION 16.0 MDR
PT_IN_VERSION 16.1 MDR
PT_IN_VERSION 17.0 MDR
PT_IN_VERSION 17.1 MDR
PT_IN_VERSION 18.0 MDR
PT_IN_VERSION 18.1 MDR
PT_IN_VERSION 19.0 MDR
PT_IN_VERSION 19.1 MDR
PT_IN_VERSION 20.0 MDR
PT_IN_VERSION 20.1 MDR
PT_IN_VERSION 8.0 MDR
PT_IN_VERSION 8.1 MDR
PT_IN_VERSION 9.0 MDR
PT_IN_VERSION 9.1 MDR
RARE_DISEASE_URL http://rarediseases.info.nih.gov/gard/7730/takayasu-arteritis/resources/1 GARD
RXAUI 3111640 RXNORM
RXAUI 3226160 RXNORM
RXAUI 3247207 RXNORM
RXAUI 3288756 RXNORM
RXAUI 3288757 RXNORM
RXAUI 3288758 RXNORM
RXAUI 3288759 RXNORM
RXAUI 3606428 RXNORM
RXCUI 1023318 RXNORM
SMQ_TERM_ADDVERSION 12.0 MDR
SMQ_TERM_CAT A MDR
SMQ_TERM_LEVEL 4 MDR
SMQ_TERM_LEVEL 5 MDR
SMQ_TERM_LMVERSION 12.0 MDR
SMQ_TERM_SCOPE 2 MDR
SMQ_TERM_STATUS A MDR
SMQ_TERM_WEIGHT 0 MDR
SNOMED_CID 239937004 NDFRT
SNOMED_CID 359789008 NDFRT
SUBSET_MEMBER 447562003~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPADVICE~ALWAYS I77.6 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPADVICE~ALWAYS M31.4 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPTARGET~I77.6 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPTARGET~M31.4 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~ALWAYS I77.6 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~ALWAYS M31.4 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~I77.6 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~M31.4 SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~X705k SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~XE2QH SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
TERMUI T040019 MSH
TERMUI T040020 MSH
TERMUI T040021 MSH
TERMUI T040022 MSH
TERMUI T683776 MSH
TERMUI T752653 MSH
TERMUI T768318 MSH
TH NLM (1975) MSH
TH NLM (1993) MSH
TH NLM (1995) MSH
TH NLM (2008) MSH
TH NLM (2010) MSH
TH NLM (2011) MSH
TH OMIM (2013) MSH
TH ORD (2010) MSH
TH UNK (19XX) MSH
TYPE_ID 900000000000003001 SNOMEDCT_US
TYPE_ID 900000000000013009 SNOMEDCT_US

Additional Concept Data:  (none)

URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0039263

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