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Kaposi Sarcoma (CUI C0036220) Suggest changes to this concept
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Terms & Properties

Concept Unique Identifier (CUI): C0036220

NCI Thesaurus Code: C9087  (see NCI Thesaurus info)

Semantic Type: Neoplastic Process

NCIt Definition: A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. The most frequent site of involvement is the skin; however it may also occur internally. It generally develops in people with compromised immune systems including those with acquired immune deficiency syndrome (AIDS).

RADLEX Definition: A multicentric, malignant neoplastic vascular proliferation characterized by the development of bluish-red cutaneous nodules, usually on the lower extremities, most often on the toes or feet, and slowly increasing in size and number and spreading to more proximal areas. The tumors have endothelium-lined channels and vascular spaces admixed with variably sized aggregates of spindle-shaped cells, and often remain confined to the skin and subcutaneous tissue, but widespread visceral involvement may occur. Kaposi's sarcoma occurs spontaneously in Jewish and Italian males in Europe and the United States. An aggressive variant in young children is endemic in some areas of Africa. A third form occurs in about 0.04% of kidney transplant patients. There is also a high incidence in aids patients. (From Dorland, 27th ed & Holland et al., Cancer Medicine, 3d ed, pp2105-7) hhv-8 is the suspected cause. [MeSH]

HPO Definition: A systemic disease which can present with cutaneous lesions with or without internal involvement. Tumors are caused by Human herpesvirus 8 (HHV8), also known as Kaposi's sarcoma-associated herpesvirus (KSHV). [HPO:sdoelken]

MEDLINEPLUS Definition: 

Kaposi's sarcoma is a cancer that causes patches of abnormal tissue to grow under the skin, in the lining of the mouth, nose, and throat or in other organs. The patches are usually red or purple and are made of cancer cells and blood cells. The red and purple patches often cause no symptoms, though they may be painful. If the cancer spreads to the digestive tract or lungs, bleeding can result. Lung tumors can make breathing hard.

Before the HIV/AIDS epidemic, KS usually developed slowly. In HIV/AIDS patients, though, the disease moves quickly. Treatment depends on where the lesions are and how bad they are. Treatment for HIV itself can shrink the lesions. However, treating KS does not improve survival from HIV/AIDS itself.

NIH: National Cancer Institute

NCI-GLOSS Definition: A type of cancer characterized by the abnormal growth of blood vessels that develop into skin lesions or occur internally.

CSP Definition: multicentric, malignant neoplastic vascular proliferation characterized by the development of bluish-red cutaneous nodules, usually on the lower extremities, most often on the toes or feet, and slowly increasing in size and number and spreading to more proximal areas; occurs spontaneously in Jewish and Italian males; aggressive variant in young children is endemic in some areas of Africa; a third form occurs in about 0.04% of kidney transplant patients; there is also a high incidence in AIDS patients; human herpesvirus 8 is the suspected cause.

MSH Definition: A multicentric, malignant neoplastic vascular proliferation characterized by the development of bluish-red cutaneous nodules, usually on the lower extremities, most often on the toes or feet, and slowly increasing in size and number and spreading to more proximal areas. The tumors have endothelium-lined channels and vascular spaces admixed with variably sized aggregates of spindle-shaped cells, and often remain confined to the skin and subcutaneous tissue, but widespread visceral involvement may occur. Kaposi's sarcoma occurs spontaneously in Jewish and Italian males in Europe and the United States. An aggressive variant in young children is endemic in some areas of Africa. A third form occurs in about 0.04% of kidney transplant patients. There is also a high incidence in AIDS patients. (From Dorland, 27th ed & Holland et al., Cancer Medicine, 3d ed, pp2105-7) HHV-8 is the suspected cause.

Synonyms & Abbreviations: (see Synonym Details)
ENDOTHELIOSARCOMA
HHV 8
HHV8
KAPOSI CANCER, SARCOMA
Kaposi sarcoma, morphology
Kaposi sarcoma
Kaposi's sarcoma (C46)
Kaposi's sarcoma (clinical)
Kaposi's sarcoma (disorder)
Kaposi's sarcoma NOS
Kaposi's sarcoma of unspecified site
Kaposi's sarcoma, morphology (morphologic abnormality)
Kaposi's sarcoma, morphology
Kaposi's sarcoma, unspecified site
Kaposi's sarcoma, unspecified
Kaposi's sarcomas
Kaposi's Sarcoma
Kaposi-Sarkom
KAPOSIS SARCOMA
KS - Kaposi's sarcoma
KS
Multiple haemorrhagic sarcoma
Multiple hemorrhagic sarcoma
Multiple idiopathic haemorrhagic sarcoma
Multiple idiopathic hemorrhagic sarcoma
Multiple Idiopathic Pigmented Hemangiosarcoma
Sarcoma, Kaposi [Disease/Finding]
Sarcoma, Kaposi's
Sarcoma, Kaposi
sarcoma, multiple hemorrhagic
SARCOMA, MULTIPLE IDIOPATHIC HEMORRHAGIC
Skin cancer, Kaposi sarcoma

External Source Codes: 
NCI Thesaurus Code C9087 (see NCI Thesaurus info)

Other Properties: Property Definitions
Name Value Source
ACTIVE 1 SNOMEDCT_US
AN coordinate IM with precoordinated organ/ neoplasm term (IM) MSH
AQL BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SE SU TH UL UR VE VI MSH
CASE_SIGNIFICANCE_ID 900000000000017005 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000448009 SNOMEDCT_US
CODE_FIRST any human immunodeficiency virus [HIV] disease (B20) ICD10CM
Contributing_Source CTRP NCI
CTV3ID BBTA. SNOMEDCT_US
CTV3ID XaBBF SNOMEDCT_US
DATE_CREATED 10/18/1999 MEDLINEPLUS
DATE_CREATED 2011-06-06T04:33:09Z HPO
DATE_LAST_MODIFIED 2016-03-30 PDQ
DC 1 MSH
DEFINITION_STATUS_ID 900000000000073002 SNOMEDCT_US
DEFINITION_STATUS_ID 900000000000074008 SNOMEDCT_US
DID 2007-1936 CSP
DX 19980101 MSH
EFFECTIVE_TIME 20020131 SNOMEDCT_US
HN 98; was SARCOMA, KAPOSI'S 1963-97; KAPOSI SARCOMA was KAPOSI'S SARCOMA 1963-97 MSH
IAN DEFAULT ICD10
ICD-O-3_Code 9140/3 NCI
ICD-O-3_CODE 9140/3 SNOMEDCT_US
ICE Viscera NOS ICD9CM
INCLUSION_TERM morphology code M9140 with behaviour code /3 ICD10
MDA 19990101 MSH
MESH_DEFINITION A multicentric, malignant neoplastic vascular proliferation characterized by the development of bluish-red cutaneous nodules, usually on the lower extremities, most often on the toes or feet, and slowly increasing in size and number and spreading to more proximal areas. The tumors have endothelium-lined channels and vascular spaces admixed with variably sized aggregates of spindle-shaped cells, and often remain confined to the skin and subcutaneous tissue, but widespread visceral involvement may occur. Kaposi's sarcoma occurs spontaneously in Jewish and Italian males in Europe and the United States. An aggressive variant in young children is endemic in some areas of Africa. A third form occurs in about 0.04% of kidney transplant patients. There is also a high incidence in AIDS patients. (From Dorland, 27th ed & Holland et al., Cancer Medicine, 3d ed, pp2105-7) HHV-8 is the suspected cause. NDFRT
MESH_DUI D012514 NDFRT
MESH_NAME Sarcoma, Kaposi NDFRT
MESH_UI M0019437 NDFRT
MMR 20120703 MSH
MN C02.256.466.860 MSH
MN C04.557.450.795.850 MSH
MN C04.557.645.750 MSH
MP_HEALTH_TOPIC_URL https://www.nlm.nih.gov/medlineplus/kaposissarcoma.html MEDLINEPLUS
MP_OTHER_LANGUAGE_URL Spanish https://www.nlm.nih.gov/medlineplus/spanish/kaposissarcoma.html MEDLINEPLUS
MP_PRIMARY_INSTITUTE_URL National Cancer Institute http://www.nci.nih.gov/ MEDLINEPLUS
NDFRT_KIND DISEASE_KIND NDFRT
Neoplastic_Status Malignant NCI
NUI N0000002676 NDFRT
ORDER_NO 01711 ICD10CM
ORDER_NO 01722 ICD10CM
ORIG_STY Neoplasm diagnosis PDQ
PID 1271 PDQ
PM 98; was SARCOMA, KAPOSI'S 1963-97; KAPOSI SARCOMA was KAPOSI'S SARCOMA 1963-97 MSH
PRIMARY_PATH 10023284$10023285$10072990$10029104$Kaposi's sarcoma$Kaposi's sarcomas$Soft tissue neoplasms malignant and unspecified$Neoplasms benign, malignant and unspecified (incl cysts and polyps) MDR
PRIMARY_SOC 10029104 MDR
PT_IN_VERSION 10.0 MDR
PT_IN_VERSION 10.1 MDR
PT_IN_VERSION 11.0 MDR
PT_IN_VERSION 11.1 MDR
PT_IN_VERSION 12.0 MDR
PT_IN_VERSION 12.1 MDR
PT_IN_VERSION 13.0 MDR
PT_IN_VERSION 13.1 MDR
PT_IN_VERSION 14.0 MDR
PT_IN_VERSION 14.1 MDR
PT_IN_VERSION 15.0 MDR
PT_IN_VERSION 15.1 MDR
PT_IN_VERSION 16.0 MDR
PT_IN_VERSION 16.1 MDR
PT_IN_VERSION 17.0 MDR
PT_IN_VERSION 17.1 MDR
PT_IN_VERSION 18.0 MDR
PT_IN_VERSION 18.1 MDR
PT_IN_VERSION 19.0 MDR
PT_IN_VERSION 19.1 MDR
PT_IN_VERSION 20.0 MDR
PT_IN_VERSION 20.1 MDR
PT_IN_VERSION 8.0 MDR
PT_IN_VERSION 8.1 MDR
PT_IN_VERSION 9.0 MDR
PT_IN_VERSION 9.1 MDR
RXAUI 3184271 RXNORM
RXAUI 3184276 RXNORM
RXAUI 3236574 RXNORM
RXAUI 3236575 RXNORM
RXAUI 4223422 RXNORM
RXCUI 1027423 RXNORM
SMQ_TERM_ADDVERSION 10.0 MDR
SMQ_TERM_ADDVERSION 12.0 MDR
SMQ_TERM_CAT A MDR
SMQ_TERM_LEVEL 4 MDR
SMQ_TERM_LEVEL 5 MDR
SMQ_TERM_LMVERSION 14.0 MDR
SMQ_TERM_LMVERSION 20.0 MDR
SMQ_TERM_SCOPE 2 MDR
SMQ_TERM_STATUS A MDR
SMQ_TERM_WEIGHT 0 MDR
SNOMED_CID 109385007 NDFRT
SUBSET_MEMBER 446608001~MAPTARGET~9140/3 SNOMEDCT_US
SUBSET_MEMBER 447562003~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPADVICE~ALWAYS C46.9 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPTARGET~C46.9 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~ALWAYS C46.9 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | DESCENDANTS NOT EXHAUSTIVELY MAPPED SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~C46.9 SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~BBTA. SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~XaBBF SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
TERM_LEVEL 4 ICDO
TERM_LEVEL Synonym ICDO
TERMUI T037132 MSH
TERMUI T037133 MSH
TERMUI T037134 MSH
TERMUI T782963 MSH
TH NLM (1966) MSH
TH NLM (1998) MSH
TH NLM (2012) MSH
TH OMIM (2013) MSH
TH ORD (2010) MSH
TH UNK (19XX) MSH
TYPE_ID 900000000000003001 SNOMEDCT_US
TYPE_ID 900000000000013009 SNOMEDCT_US

Additional Concept Data:  (none)

URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0036220

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