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Henoch-Schoenlein Purpura (CUI C0034152) Suggest changes to this concept
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Terms & Properties

Concept Unique Identifier (CUI): C0034152

NCI Thesaurus Code: C34963  (see NCI Thesaurus info)

Semantic Type: Disease or Syndrome

NCIt Definition: A systemic, usually self-limited immune complex vasculitis, characterized by immunoglobulin A deposition in the small vessels and kidneys. It is manifested with small hemorrhages in the skin, gastrointestinal symptoms, arthritis, and nephropathy.

GARD Definition: Henoch-Schonlein purpura (HSP) is a disease that involves purple spots on the skin (purpura), joint pain, digestive problems, and glomerulonephritis (a type of kidney disorder).  While the cause of this condition is not fully understood, it may develop as an immune response to an infection.  HSP is usually seen in children, but it may affect people of any age. Most cases go away on their own without treatment.  For those cases which require treatment, the main goal is to relieve symptoms such as joint pain, abdominal pain, or swelling. In many cases, over-the-counter medicines can be used. In some patients with severe arthritis, prednisone, a steroid medicine, may be prescribed. - this information is from GARD/ORDR/NCATS.

NICHD Definition: A systemic, usually self-limited immune complex vasculitis, characterized by immunoglobulin A deposition in the small vessels and kidneys. It is manifested with small hemorrhages in the skin, gastrointestinal symptoms, arthritis, and nephropathy.

MSH Definition: A systemic non-thrombocytopenic purpura caused by HYPERSENSITIVITY VASCULITIS and deposition of IGA-containing IMMUNE COMPLEXES within the blood vessels throughout the body, including those in the kidney (KIDNEY GLOMERULUS). Clinical symptoms include URTICARIA; ERYTHEMA; ARTHRITIS; GASTROINTESTINAL HEMORRHAGE; and renal involvement. Most cases are seen in children after acute upper respiratory infections.

Synonyms & Abbreviations: (see Synonym Details)
Acute vascular purpura
Allergic purpura
Allergic vascular purpura
Anaphylactic vascular purpura
Anaphylactoid purpura
Anaphylactoid vascular purpura
Autoimmune purpura
Henoch Purpura
Henoch Schoenlein Purpura
Henoch Schonlein Purpuras
HENOCH SCHONLEIN PURPURA
HENOCH SCHONLEIN SYNDROME
Henoch Shonlein purpura
Henoch's purpura
HENOCH-SCHOENLEIN PURPURA
Henoch-Schoenlein vasculitis
Henoch-Scholein purpura
Henoch-Schonlein Purpuras
Henoch-Schonlein purpura
Henoch-Schonlein
Henoch-Schönlein purpura
Henoch-Schönlein purpura (disorder)
Henoch-schönlein purpura
HSP - Henoch-Schonlein purpura
HSP
IgA vasculitis
Immunoglobulin A vasculitis
PURPURA ALLERGIC
Purpura anaphylactoid
Purpura Henoch(-Schönlein)
Purpura vascular allergic
PURPURA, ALLERGIC
Purpura, Anaphylactoid
Purpura, autoimmune
Purpura, Henoch Schonlein
Purpura, Henoch's
Purpura, Henoch-Schoenlein
Purpura, Henoch-Schonlein
Purpura, Henoch
Purpura, Schoenlein Henoch
Purpura, Schoenlein-Henoch [Disease/Finding]
Purpura, Schoenlein-Henoch
Purpura, Schonlein Henoch
Purpura, Schonlein-Henoch
Purpuras, Henoch Schonlein
Purpuras, Henoch-Schonlein
Purpuras, Schonlein-Henoch
Schoenlein Henoch Purpura
Schoenlein-Henoch purpura
Schonlein Purpura, Henoch
Schonlein Purpuras, Henoch
Schonlein-Henoch Purpuras
Schonlein-Henoch Purpura
Spring fever

External Source Codes: 
NCI Thesaurus Code C34963 (see NCI Thesaurus info)

Other Properties: Property Definitions
Name Value Source
ACTIVE 1 SNOMEDCT_US
AN nonthrombopenic: thrombopenic = PURPURA, THROMBOCYTOPENIC MSH
AQL BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI MSH
CASE_SIGNIFICANCE_ID 900000000000017005 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000448009 SNOMEDCT_US
CHARACTERISTIC_TYPE_ID 900000000000011006 SNOMEDCT_US
Contributing_Source MedDRA NCI
Contributing_Source NICHD NCI
CTV3ID D3100 SNOMEDCT_US
DATE_CREATED 2013-01-09T00:04:00 GARD
DATE_CREATED 2015-01-22T00:04:00 GARD
DATE_LAST_MODIFIED 2013-01-09T00:04:00 GARD
DC 1 MSH
DEFINITION_STATUS_ID 900000000000074008 SNOMEDCT_US
DID 4006-0049 CSP
DISEASE_IDENTIFIER_ID 288 GARD
DISEASE_IDENTIFIER_ID 289 GARD
DISEASE_IDENTIFIER_ID 291 GARD
DISEASE_IDENTIFIER_ID 33801 GARD
DISEASE_IDENTIFIER_ID 33802 GARD
DISEASE_IDENTIFIER_ID 33803 GARD
DX 19750901 MSH
EFFECTIVE_TIME 20020131 SNOMEDCT_US
EXCLUDES1 thrombocytopenic hemorrhagic purpura (D69.3) ICD10CM
HAS_GARD_PAGE true GARD
HN 75 MSH
IAN DEFAULT ICD10
ICE Peliosis rheumatica; Purpura: {anaphylactoid; autoimmune; Henoch's; nonthrombocytopenic: {hemorrhagic; idiopathic}; rheumatica; Schonlein-Henoch; vascular}; Vasculitis, allergic ICD9CM
IDENTIFIER_SOURCE Orp GARD
IDENTIFIER_TYPE_ID 1 GARD
INCLUSION_TERM Purpura: anaphylactoid ICD10
INCLUSION_TERM Purpura: Henoch(-Schönlein) ICD10
INCLUSION_TERM Purpura: nonthrombocytopenic: haemorrhagic ICD10
INCLUSION_TERM Purpura: nonthrombocytopenic: idiopathic ICD10
INCLUSION_TERM Purpura: vascular ICD10
INCLUSION_TERM Vasculitis, allergic ICD10
IS_ACTIVE true GARD
IS_RARE true GARD
IS_SPANISH false GARD
LAST_REVIEW_DATE 2007-02-08T00:00:00 GARD
MDA 19741111 MSH
MESH_DEFINITION A systemic non-thrombocytopenic purpura caused by HYPERSENSITIVITY VASCULITIS and deposition of IGA-containing IMMUNE COMPLEXES within the blood vessels throughout the body, including those in the kidney (KIDNEY GLOMERULUS). Clinical symptoms include URTICARIA; ERYTHEMA; ARTHRITIS; GASTROINTESTINAL HEMORRHAGE; and renal involvement. Most cases are seen in children after acute upper respiratory infections. NDFRT
MESH_DUI D011695 NDFRT
MESH_NAME Purpura, Schoenlein-Henoch NDFRT
MESH_UI M0018180 NDFRT
MMR 20100625 MSH
MN C14.907.940.777 MSH
MN C15.378.100.802.375 MSH
MN C15.378.463.515.580 MSH
MN C20.543.520.600 MSH
MN C23.550.414.950.375 MSH
MN C23.888.885.687.375 MSH
MODIFIER_ID 900000000000451002 SNOMEDCT_US
NDFRT_KIND DISEASE_KIND NDFRT
NICHD_Hierarchy_Term Henoch-Schönlein Purpura NCI
NUI N0000002555 NDFRT
ORDER_NO 03473 ICD10CM
PM 75 MSH
PRIMARY_PATH 10019617$10037555$10047043$10040785$Henoch-Schonlein purpura$Purpura and related conditions$Skin vascular abnormalities$Skin and subcutaneous tissue disorders MDR
PRIMARY_SOC 10040785 MDR
PT_IN_VERSION 10.0 MDR
PT_IN_VERSION 10.1 MDR
PT_IN_VERSION 11.0 MDR
PT_IN_VERSION 11.1 MDR
PT_IN_VERSION 12.0 MDR
PT_IN_VERSION 12.1 MDR
PT_IN_VERSION 13.0 MDR
PT_IN_VERSION 13.1 MDR
PT_IN_VERSION 14.0 MDR
PT_IN_VERSION 14.1 MDR
PT_IN_VERSION 15.0 MDR
PT_IN_VERSION 15.1 MDR
PT_IN_VERSION 16.0 MDR
PT_IN_VERSION 16.1 MDR
PT_IN_VERSION 17.0 MDR
PT_IN_VERSION 17.1 MDR
PT_IN_VERSION 18.0 MDR
PT_IN_VERSION 18.1 MDR
PT_IN_VERSION 19.0 MDR
PT_IN_VERSION 19.1 MDR
PT_IN_VERSION 20.0 MDR
PT_IN_VERSION 20.1 MDR
PT_IN_VERSION 8.0 MDR
PT_IN_VERSION 8.1 MDR
PT_IN_VERSION 9.0 MDR
PT_IN_VERSION 9.1 MDR
RARE_DISEASE_URL http://rarediseases.info.nih.gov/gard/8204/henoch-schonlein-purpura/resources/1 GARD
REF orcid.org/0000-0001-6908-9849 HPO
RXAUI 3107725 RXNORM
RXAUI 3108801 RXNORM
RXAUI 3172061 RXNORM
RXAUI 3172063 RXNORM
RXAUI 3226310 RXNORM
RXAUI 3226311 RXNORM
RXAUI 3236801 RXNORM
RXAUI 3287459 RXNORM
RXAUI 3287460 RXNORM
RXAUI 3288499 RXNORM
RXCUI 1021763 RXNORM
SMQ_TERM_ADDVERSION 12.0 MDR
SMQ_TERM_ADDVERSION 16.0 MDR
SMQ_TERM_ADDVERSION 9.0 MDR
SMQ_TERM_CAT A MDR
SMQ_TERM_LEVEL 4 MDR
SMQ_TERM_LEVEL 5 MDR
SMQ_TERM_LMVERSION 12.0 MDR
SMQ_TERM_LMVERSION 16.0 MDR
SMQ_TERM_SCOPE 2 MDR
SMQ_TERM_STATUS A MDR
SMQ_TERM_WEIGHT 0 MDR
SNOMED_CID 191306005 NDFRT
SNOMED_CID 21148002 NDFRT
SOS Excludes: hemorrhagic purpura (287.39); purpura annularis telangiectodes (709.1) ICD9CM
SUBSET_MEMBER 447562003~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPADVICE~ALWAYS D69.0 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPTARGET~D69.0 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~ALWAYS D69.0 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~D69.0 SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~D3100 SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
TERMUI T034571 MSH
TERMUI T034572 MSH
TERMUI T034573 MSH
TERMUI T034574 MSH
TERMUI T034575 MSH
TERMUI T034579 MSH
TERMUI T750975 MSH
TERMUI T750976 MSH
TERMUI T750977 MSH
TH NLM (1975) MSH
TH NLM (1999) MSH
TH NLM (2010) MSH
TH ORD (2010) MSH
TH UNK (19XX) MSH
TYPE_ID 900000000000003001 SNOMEDCT_US
TYPE_ID 900000000000013009 SNOMEDCT_US

Additional Concept Data:  (none)

URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0034152

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