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Polyarteritis Nodosa (CUI C0031036) Suggest changes to this concept
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Terms & Properties

Concept Unique Identifier (CUI): C0031036

NCI Thesaurus Code: C26847  (see NCI Thesaurus info)

Semantic Type: Disease or Syndrome

NCIt Definition: A necrotizing vasculitis that affects medium-sized arteries, it is usually idiopathic, and may be triggered by viral infections (Hepatitis B, also others). A multisystem disease, it most commonly affects skin (nodules, livedo reticularis) and peripheral nerves; higher morbidity is associated with gastrointestinal, central nervous system, cardiac, and/or other organ involvement. Anti-neutrophil cytoplasmic antibodies (ANCA) are typically negative.

RADLEX Definition: A form of necrotizing vasculitis involving small- and medium-sized arteries. The signs and symptoms result from infarction and scarring of the affected organ system. [MeSH]

GARD Definition: Polyarteritis nodosa is a serious blood vessel disease in which medium-sized arteries become swollen and damaged. It occurs when certain immune cells attack the affected arteries preventing vital oxygen and nourishment. Signs and symptoms may include fever, fatigue, weakness, loss of appetite, weight loss, muscle and joint aches, and abdominal pain. The skin may show rashes, swelling, ulcers, and lumps. When nerve cells are involved numbness, pain, burning, and weakness may be present. Polyarteritis nodosa can cause serious health complications including strokes, seizures, and kidney failure. Treatment often includes steroids and other drugs to suppress the immune system. - this information is from GARD/ORDR/NCATS.

NICHD Definition: A necrotizing vasculitis that affects medium-sized arteries, it is usually idiopathic, and may be triggered by viral infections (Hepatitis B, also others). A multisystem disease, it most commonly affects skin (nodules, livedo reticularis) and peripheral nerves; higher morbidity is associated with gastrointestinal, central nervous system, cardiac, and/or other organ involvement. Anti-neutrophil cytoplasmic antibodies (ANCA) are typically negative.

CSP Definition: form of necrotizing vasculitis involving small- and medium-sized arteries; signs and symptoms result from infarction and scarring of the affected organ system.

MSH Definition: A form of necrotizing non-granulomatous inflammation occurring primarily in medium-sized ARTERIES, often with microaneurysms. It is characterized by muscle, joint, and abdominal pain resulting from arterial infarction and scarring in affected organs. Polyarteritis nodosa with lung involvement is called CHURG-STRAUSS SYNDROME.

Synonyms & Abbreviations: (see Synonym Details)
Classic Polyarteritis Nodosa
Classical Polyarteritis Nodosa
KUSSMAUL DISEASE
Kussmaul's disease
Küssmaul-Maier disease
PAN - Polyarteritis nodosa
Panarteritis nodosa
PAN
Periarteritis Nodosa
Polyarteritis nodosa (disorder)
Polyarteritis Nodosa [Disease/Finding]
POLYARTERITIS NODOSA SYSTEMIC
Polyarteritis Nodosa
Polyarteritis nodosum

External Source Codes: 
NCI Thesaurus Code C26847 (see NCI Thesaurus info)

Other Properties: Property Definitions
Name Value Source
ACTIVE 1 SNOMEDCT_US
AQL BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI MSH
CASE_SIGNIFICANCE_ID 900000000000017005 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000020002 SNOMEDCT_US
CHARACTERISTIC_TYPE_ID 900000000000011006 SNOMEDCT_US
Contributing_Source NICHD NCI
CTV3ID .G881 SNOMEDCT_US
DATE_CREATED 2013-01-09T00:04:00 GARD
DATE_CREATED 2015-01-22T00:04:00 GARD
DATE_LAST_MODIFIED 2013-01-09T00:04:00 GARD
DC 1 MSH
DEFINITION_STATUS_ID 900000000000074008 SNOMEDCT_US
DID 0571-9158 CSP
DISEASE_IDENTIFIER_ID 33813 GARD
DISEASE_IDENTIFIER_ID 33814 GARD
DISEASE_IDENTIFIER_ID 5325 GARD
DX 19950101 MSH
EFFECTIVE_TIME 20030731 SNOMEDCT_US
FX D020293 MSH
HAS_GARD_PAGE true GARD
HN 1995; was PERIARTERITIS NODOSA 1963-1994; for POLYARTERITIS NODOSA use PERIARTERITIS NODOSA 1968-1994 MSH
IAN DEFAULT ICD10
ICE Disseminated necrotizing periarteritis; Necrotizing angiitis; Panarteritis (nodosa); Periarteritis (nodosa) ICD9CM
IDENTIFIER_SOURCE Orp GARD
IDENTIFIER_TYPE_ID 1 GARD
IS_ACTIVE true GARD
IS_RARE true GARD
IS_SPANISH false GARD
LAST_REVIEW_DATE 2010-01-21T00:00:00 GARD
MDA 19990101 MSH
MESH_DEFINITION A form of necrotizing non-granulomatous inflammation occurring primarily in medium-sized ARTERIES, often with microaneurysms. It is characterized by muscle, joint, and abdominal pain resulting from arterial infarction and scarring in affected organs. Polyarteritis nodosa with lung involvement is called CHURG-STRAUSS SYNDROME. NDFRT
MESH_DUI D010488 NDFRT
MESH_NAME Polyarteritis Nodosa NDFRT
MESH_UI M0016293 NDFRT
MMR 20150623 MSH
MN C14.907.940.090.720 MSH
MN C14.907.940.897.500 MSH
MN C17.800.862.625 MSH
MODIFIER_ID 900000000000451002 SNOMEDCT_US
NDFRT_KIND DISEASE_KIND NDFRT
NICHD_Hierarchy_Term Polyarteritis Nodosa NCI
NUI N0000002359 NDFRT
OL use POLYARTERITIS NODOSA to search PERIARTERITIS NODOSA 1966-94; MSH
ORDER_NO 17926 ICD10CM
PM 1995; was PERIARTERITIS NODOSA 1963-1994; for POLYARTERITIS NODOSA see PERIARTERITIS NODOSA 1968-1994 MSH
PRIMARY_PATH 10036024$10047113$10047116$10047065$Polyarteritis nodosa$Vasculitides NEC$Vascular inflammations$Vascular disorders MDR
PRIMARY_SOC 10047065 MDR
PT_IN_VERSION 10.0 MDR
PT_IN_VERSION 10.1 MDR
PT_IN_VERSION 11.0 MDR
PT_IN_VERSION 11.1 MDR
PT_IN_VERSION 12.0 MDR
PT_IN_VERSION 12.1 MDR
PT_IN_VERSION 13.0 MDR
PT_IN_VERSION 13.1 MDR
PT_IN_VERSION 14.0 MDR
PT_IN_VERSION 14.1 MDR
PT_IN_VERSION 15.0 MDR
PT_IN_VERSION 15.1 MDR
PT_IN_VERSION 16.0 MDR
PT_IN_VERSION 16.1 MDR
PT_IN_VERSION 17.0 MDR
PT_IN_VERSION 17.1 MDR
PT_IN_VERSION 18.0 MDR
PT_IN_VERSION 18.1 MDR
PT_IN_VERSION 19.0 MDR
PT_IN_VERSION 19.1 MDR
PT_IN_VERSION 8.0 MDR
PT_IN_VERSION 8.1 MDR
PT_IN_VERSION 9.0 MDR
PT_IN_VERSION 9.1 MDR
RARE_DISEASE_URL http://rarediseases.info.nih.gov/gard/7360/polyarteritis-nodosa/resources/1 GARD
RARE_DISEASE_URL http://rarediseases.info.nih.gov/gard/7414/periarteritis-nodosa/resources/1 GARD
RXAUI 3219109 RXNORM
RXAUI 3221985 RXNORM
RXAUI 3221986 RXNORM
RXCUI 988077 RXNORM
SMQ_TERM_ADDVERSION 12.0 MDR
SMQ_TERM_ADDVERSION 9.0 MDR
SMQ_TERM_CAT A MDR
SMQ_TERM_CAT C MDR
SMQ_TERM_LEVEL 4 MDR
SMQ_TERM_LEVEL 5 MDR
SMQ_TERM_LMVERSION 12.0 MDR
SMQ_TERM_LMVERSION 9.0 MDR
SMQ_TERM_SCOPE 1 MDR
SMQ_TERM_SCOPE 2 MDR
SMQ_TERM_STATUS A MDR
SMQ_TERM_WEIGHT 0 MDR
SNOMED_CID 155441006 NDFRT
SNOMEDID R-F5E6F SNOMEDCT_US
SUBSET_MEMBER 447562003~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPADVICE~ALWAYS M30.0 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPTARGET~M30.0 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~ALWAYS M30.0 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~IF AGE AT ONSET OF CLINICAL FINDING BETWEEN 1.0 YEAR AND 18.0 YEARS CHOOSE M30.2 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~IF MICROSCOPIC POLYARTERITIS NODOSA CHOOSE M31.7 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~IF POLYARTERITIS NODOSA WITH MULTI-ORGAN INVOLVEMENT AND IF AGE AT ONSET OF CLINICAL FINDING BETWEEN 1.0 YEAR AND 18.0 YEARS CHOOSE M30.2 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~IF POLYARTERITIS NODOSA WITH MULTI-ORGAN INVOLVEMENT CHOOSE M30.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~IF POLYARTERITIS NODOSA WITH SINGLE ORGAN INVOLVEMENT AND IF AGE AT ONSET OF CLINICAL FINDING BETWEEN 1.0 YEAR AND 18.0 YEARS CHOOSE M30.2 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~IF POLYARTERITIS NODOSA WITH SINGLE ORGAN INVOLVEMENT CHOOSE M30.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447639009 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~2 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~3 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~4 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~5 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~6 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~7 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~IFA 239925001 | Polyarteritis nodosa with single organ involvement (disorder) | AND IFA 445518008 | Age at onset of clinical finding (observable entity) | >= 1.0 year AND IFA 445518008 | Age at onset of clinical finding (observable entity) | < 18.0 years SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~IFA 239925001 | Polyarteritis nodosa with single organ involvement (disorder) | SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~IFA 239927009 | Polyarteritis nodosa with multi-organ involvement (disorder) | AND IFA 445518008 | Age at onset of clinical finding (observable entity) | >= 1.0 year AND IFA 445518008 | Age at onset of clinical finding (observable entity) | < 18.0 years SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~IFA 239927009 | Polyarteritis nodosa with multi-organ involvement (disorder) | SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~IFA 239928004 | Microscopic polyarteritis nodosa (disorder) | SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~IFA 445518008 | Age at onset of clinical finding (observable entity) | >= 1.0 year AND IFA 445518008 | Age at onset of clinical finding (observable entity) | < 18.0 years SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~OTHERWISE TRUE SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~M30.0 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~M30.2 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~M31.7 SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~.G881 SNOMEDCT_US
SUBSET_MEMBER 900000000000498005~MAPTARGET~R-F5E6F SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
TERMUI T030994 MSH
TERMUI T030995 MSH
TH NLM (1966) MSH
TH NLM (1995) MSH
TYPE_ID 900000000000003001 SNOMEDCT_US
TYPE_ID 900000000000013009 SNOMEDCT_US

Additional Concept Data:  (none)

URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0031036

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