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Terms & Properties |
Concept Unique Identifier (CUI): C0020541
NCI Thesaurus Code: C3119 (see NCI Thesaurus info)
Semantic Type: Disease or Syndrome
NCIt Definition: Increased blood pressure in the portal venous system. It is most commonly caused by cirrhosis. Other causes include portal vein thrombosis, Budd-Chiari syndrome, and right heart failure. Complications include ascites, esophageal varices, encephalopathy, and splenomegaly.
GARD Definition: Portal hypertension is abnormally high blood pressure in branches of the portal vein, the large vein that brings blood from the intestine to the liver. Portal hypertension itself does not cause symptoms, but complications from the condition can lead to an enlarged abdomen, abdominal discomfort, confusion, drowsiness and internal bleeding. It may be caused by a variety of conditions, but cirrhosis is the most common cause in Western countries. Treatment is generally directed toward the cause of the condition, although emergency treatment is sometimes needed for serious complications. - this information is from GARD/ORDR/NCATS.
HPO Definition: Increased pressure in the portal vein. [HPO:probinson]
CTCAE Definition: A disorder characterized by an increase in blood pressure in the portal venous system.
NCI-GLOSS Definition: High blood pressure in the vein that carries blood to the liver from the stomach, small and large intestines, spleen, pancreas, and gallbladder. It is usually caused by a block in the blood flow through the liver due to cirrhosis (scarring) of the liver.
NICHD Definition: Increased blood pressure in the portal venous system which manifests as ascites, splenomegaly and/or varices.
CSP Definition: abnormally increased pressure in the portal venous system, frequently seen in cirrhosis of the liver and other conditions causing obstruction of the portal vein.
MSH Definition: Abnormal increase of resistance to blood flow within the hepatic PORTAL SYSTEM, frequently seen in LIVER CIRRHOSIS and conditions with obstruction of the PORTAL VEIN.
Synonyms & Abbreviations: (see Synonym Details)
HYPERTENSION PORTAL |
Hypertension, Portal [Disease/Finding] |
HYPERTENSION, PORTAL |
Hypertensions, Portal |
PHT - Portal hypertension |
Portal hypertension (disorder) |
Portal hypertensions |
portal hypertension |
External Source Codes:
NCI Thesaurus Code | C3119 (see NCI Thesaurus info) |
Name | Value | Source |
---|---|---|
ACTIVE | 1 | SNOMEDCT_US |
AQL | BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI | MSH |
CASE_SIGNIFICANCE_ID | 900000000000017005 | SNOMEDCT_US |
CASE_SIGNIFICANCE_ID | 900000000000448009 | SNOMEDCT_US |
Contributing_Source | MedDRA | NCI |
Contributing_Source | NICHD | NCI |
CTV3ID | J623. | SNOMEDCT_US |
DATE_CREATED | 2013-01-09T00:04:00 | GARD |
DATE_LAST_MODIFIED | 2013-01-09T00:04:00 | GARD |
DC | 1 | MSH |
DEFINITION_STATUS_ID | 900000000000074008 | SNOMEDCT_US |
DID | 1754-2142 | CSP |
DISEASE_IDENTIFIER_ID | 330 | GARD |
DX | 19600101 | MSH |
EFFECTIVE_TIME | 20020131 | SNOMEDCT_US |
FX | D011170 | MSH |
HAS_GARD_PAGE | true | GARD |
HN | CRUVEILHIER-BAUMGARTEN SYNDROME was heading 1975-96 (see under HYPERTENSION, PORTAL 1979-90, see under LIVER CIRRHOSIS 1975-78); was see under LIVER CIRRHOSIS 1963-74 | MSH |
HN | ETOH descriptor 2000. | AOD |
HPO_COMMENT | Portal hypertension is defined as portal vein pressures exceeding 5 mm Hg or portal vein to hepatic vein gradient of greater than 10 mm Hg. | HPO |
IAN | DEFAULT | ICD10 |
ICA | Use additional code for any associated complications, such as: portal hypertensive gastropathy (537.89) | ICD9CM |
IDENTIFIER_TYPE_ID | 1 | GARD |
IS_ACTIVE | true | GARD |
IS_RARE | false | GARD |
IS_SPANISH | false | GARD |
MDA | 19990101 | MSH |
MESH_DEFINITION | Abnormal increase of resistance to blood flow within the hepatic PORTAL SYSTEM, frequently seen in LIVER CIRRHOSIS and conditions with obstruction of the PORTAL VEIN. | NDFRT |
MESH_DUI | D006975 | NDFRT |
MESH_NAME | Hypertension, Portal | NDFRT |
MESH_UI | M0010863 | NDFRT |
MMR | 20040707 | MSH |
MN | C06.552.494 | MSH |
NDFRT_KIND | DISEASE_KIND | NDFRT |
NICHD_Hierarchy_Term | Portal Hypertension | NCI |
NUI | N0000001618 | NDFRT |
OL | use LIVER CIRRHOSIS to search CRUVEILHIER-BAUMGARTEN SYNDROME 1966-74 | MSH |
ORDER_NO | 13599 | ICD10CM |
PM | CRUVEILHIER-BAUMGARTEN SYNDROME was heading 1975-96 (see under HYPERTENSION, PORTAL 1979-90, see under LIVER CIRRHOSIS 1975-78); was see under LIVER CIRRHOSIS 1963-74 | MSH |
PRIMARY_PATH | 10036200$10019712$10019654$10019805$Portal hypertension$Hepatic vascular disorders$Hepatic and hepatobiliary disorders$Hepatobiliary disorders | MDR |
PRIMARY_SOC | 10019805 | MDR |
PT_IN_VERSION | 10.0 | MDR |
PT_IN_VERSION | 10.1 | MDR |
PT_IN_VERSION | 11.0 | MDR |
PT_IN_VERSION | 11.1 | MDR |
PT_IN_VERSION | 12.0 | MDR |
PT_IN_VERSION | 12.1 | MDR |
PT_IN_VERSION | 13.0 | MDR |
PT_IN_VERSION | 13.1 | MDR |
PT_IN_VERSION | 14.0 | MDR |
PT_IN_VERSION | 14.1 | MDR |
PT_IN_VERSION | 15.0 | MDR |
PT_IN_VERSION | 15.1 | MDR |
PT_IN_VERSION | 16.0 | MDR |
PT_IN_VERSION | 16.1 | MDR |
PT_IN_VERSION | 17.0 | MDR |
PT_IN_VERSION | 17.1 | MDR |
PT_IN_VERSION | 18.0 | MDR |
PT_IN_VERSION | 18.1 | MDR |
PT_IN_VERSION | 19.0 | MDR |
PT_IN_VERSION | 19.1 | MDR |
PT_IN_VERSION | 20.0 | MDR |
PT_IN_VERSION | 20.1 | MDR |
PT_IN_VERSION | 8.0 | MDR |
PT_IN_VERSION | 8.1 | MDR |
PT_IN_VERSION | 9.0 | MDR |
PT_IN_VERSION | 9.1 | MDR |
RARE_DISEASE_URL | http://rarediseases.info.nih.gov/gard/8229/portal-hypertension/resources/1 | GARD |
RXAUI | 3174583 | RXNORM |
RXAUI | 3174584 | RXNORM |
RXCUI | 1021793 | RXNORM |
SMQ_TERM_ADDVERSION | 10.1 | MDR |
SMQ_TERM_ADDVERSION | 8.0 | MDR |
SMQ_TERM_CAT | A | MDR |
SMQ_TERM_LEVEL | 4 | MDR |
SMQ_TERM_LEVEL | 5 | MDR |
SMQ_TERM_LMVERSION | 12.1 | MDR |
SMQ_TERM_LMVERSION | 19.0 | MDR |
SMQ_TERM_SCOPE | 1 | MDR |
SMQ_TERM_SCOPE | 2 | MDR |
SMQ_TERM_STATUS | A | MDR |
SMQ_TERM_STATUS | I | MDR |
SMQ_TERM_WEIGHT | 0 | MDR |
SNOMED_CID | 34742003 | NDFRT |
SUBSET_MEMBER | 447562003~CORRELATIONID~447561005 | SNOMEDCT_US |
SUBSET_MEMBER | 447562003~MAPADVICE~ALWAYS K76.6 | SNOMEDCT_US |
SUBSET_MEMBER | 447562003~MAPCATEGORYID~447637006 | SNOMEDCT_US |
SUBSET_MEMBER | 447562003~MAPGROUP~1 | SNOMEDCT_US |
SUBSET_MEMBER | 447562003~MAPPRIORITY~1 | SNOMEDCT_US |
SUBSET_MEMBER | 447562003~MAPRULE~TRUE | SNOMEDCT_US |
SUBSET_MEMBER | 447562003~MAPTARGET~K76.6 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~CORRELATIONID~447561005 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPADVICE~ALWAYS K76.6 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPADVICE~IF CRUVEILHIER-BAUMGARTEN SYNDROME CHOOSE K74.69 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPADVICE~IF PORTAL HYPERTENSION CAUSED BY ANTIRETROVIRAL DRUG CHOOSE T37.5X5? | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | EPISODE OF CARE INFORMATION NEEDED | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPADVICE~IF PORTAL HYPERTENSION DUE TO CYSTIC FIBROSIS CHOOSE E84.8 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPADVICE~IF PORTAL HYPERTENSION DUE TO CYSTIC FIBROSIS CHOOSE K76.6 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPADVICE~MAP SOURCE CONCEPT CANNOT BE CLASSIFIED WITH AVAILABLE DATA | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPCATEGORYID~447637006 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPCATEGORYID~447638001 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPCATEGORYID~447639009 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPGROUP~1 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPGROUP~2 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPPRIORITY~1 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPPRIORITY~2 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPPRIORITY~3 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPRULE~IFA 45256007 | Cruveilhier-Baumgarten syndrome | | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPRULE~IFA 707420003 | Portal hypertension due to cystic fibrosis | | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPRULE~IFA 713542007 | Portal hypertension caused by antiretroviral drug | | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPRULE~OTHERWISE TRUE | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPTARGET~E84.8 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPTARGET~K74.69 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPTARGET~K76.6 | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPTARGET~T37.5X5? | SNOMEDCT_US |
SUBSET_MEMBER | 6011000124106~MAPTARGET~ | SNOMEDCT_US |
SUBSET_MEMBER | 900000000000497000~MAPTARGET~J623. | SNOMEDCT_US |
SUBSET_MEMBER | 900000000000508004~ACCEPTABILITYID~900000000000548007 | SNOMEDCT_US |
SUBSET_MEMBER | 900000000000508004~ACCEPTABILITYID~900000000000549004 | SNOMEDCT_US |
SUBSET_MEMBER | 900000000000509007~ACCEPTABILITYID~900000000000548007 | SNOMEDCT_US |
SUBSET_MEMBER | 900000000000509007~ACCEPTABILITYID~900000000000549004 | SNOMEDCT_US |
TERMUI | T020941 | MSH |
TH | NLM (1966) | MSH |
TYPE_ID | 900000000000003001 | SNOMEDCT_US |
TYPE_ID | 900000000000013009 | SNOMEDCT_US |
USE_ADDITIONAL | code for any associated complications, such as: | ICD10CM |
USE_ADDITIONAL | portal hypertensive gastropathy (K31.89) | ICD10CM |
Additional Concept Data: (none)
URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0020541