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Churg-Strauss Syndrome (CUI C0008728) Suggest changes to this concept
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Terms & Properties

Concept Unique Identifier (CUI): C0008728

NCI Thesaurus Code: C34481  (see NCI Thesaurus info)

Semantic Type: Disease or Syndrome

NCIt Definition: An autoimmune necrotizing vasculitis with the formation of granulomas. It is a pulmonary and systemic vasculitis associated with eosinophilia.

GARD Definition: Churg Strauss syndrome is a condition characterized by asthma, high levels of eosinophils (a type of white blood cell that helps fight infection), and inflammation of small to medium sized blood vessels (vasculitis). The inflamed vessels can affect various organ systems including the lungs, gastrointestinal tract, skin, heart and nervous system. The exact cause of Churg Strauss syndrome is unknown, but it is thought to be an autoimmune disorder. Treatment may involve the use of glucocorticoids and/or other immunosuppressive therapies. - this information is from GARD/ORDR/NCATS.

MSH Definition: Widespread necrotizing angiitis with granulomas. Pulmonary involvement is frequent. Asthma or other respiratory infection may precede evidence of vasculitis. Eosinophilia and lung involvement differentiate this disease from POLYARTERITIS NODOSA.

Synonyms & Abbreviations: (see Synonym Details)
Allergic Angiitides, Granulomatous
Allergic Angiitides
Allergic angiitis and granulomatosis
Allergic Angiitis, Granulomatous
Allergic angiitis
Allergic Granulomatoses
Allergic granulomatosis angiitis (disorder)
Allergic granulomatosis angiitis
ALLERGIC GRANULOMATOSIS OF CHURG-STRAUSS
Allergic granulomatosis
Allergic granulomatous and angiitis
Allergic Granulomatous Angiitides
Allergic granulomatous angiitis
Angiitides, Allergic Granulomatous
Angiitides, Allergic
Angiitides, Granulomatous Allergic
ANGIITIS, ALLERGIC GRANULOMATOUS
ANGIITIS, ALLERGIC
Angiitis, Granulomatous Allergic
Churg Strauss syndrome
Churg-Strauss Syndrome [Disease/Finding]
CHURG-STRAUSS SYNDROME
Churg-Strauss vasculitis
CSS - Churg-Strauss syndrome
CSS
EGPA - eosinophilic granulomatosis with polyangiitis
EGPA
Eosinophilic granulomatosis with polyangiitis
Eosinophilic Granulomatous Vasculitides
Eosinophilic granulomatous vasculitis
Granulomatoses, Allergic
Granulomatosis, Allergic
Granulomatous Allergic Angiitides
Granulomatous allergic angiitis
Granulomatous Angiitides, Allergic
Granulomatous Angiitis, Allergic
Granulomatous Vasculitides, Eosinophilic
Granulomatous Vasculitis, Eosinophilic
Polyarteritis with lung involvement [Churg-Strauss]
Syndrome, Churg-Strauss
Vasculitides, Eosinophilic Granulomatous
Vasculitis, Churg Strauss
Vasculitis, Churg-Strauss
Vasculitis, Eosinophilic Granulomatous

External Source Codes: 
NCI Thesaurus Code C34481 (see NCI Thesaurus info)

Other Properties: Property Definitions
Name Value Source
ACTIVE 1 SNOMEDCT_US
AQL BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI MSH
CASE_SIGNIFICANCE_ID 900000000000017005 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000448009 SNOMEDCT_US
CHARACTERISTIC_TYPE_ID 900000000000011006 SNOMEDCT_US
CTV3ID X705i SNOMEDCT_US
DATE_CREATED 2013-01-09T00:04:00 GARD
DATE_CREATED 2015-01-09T00:03:00 GARD
DATE_LAST_MODIFIED 2013-01-09T00:04:00 GARD
DATE_LAST_MODIFIED 2015-01-09T00:03:00 GARD
DC 1 MSH
DEFINITION_STATUS_ID 900000000000073002 SNOMEDCT_US
DISEASE_IDENTIFIER_ID 17886 GARD
DISEASE_IDENTIFIER_ID 17887 GARD
DISEASE_IDENTIFIER_ID 17888 GARD
DISEASE_IDENTIFIER_ID 17889 GARD
DISEASE_IDENTIFIER_ID 17890 GARD
DISEASE_IDENTIFIER_ID 17891 GARD
DISEASE_IDENTIFIER_ID 17892 GARD
DISEASE_IDENTIFIER_ID 29505 GARD
DISEASE_IDENTIFIER_ID 29506 GARD
DISEASE_IDENTIFIER_ID 29507 GARD
DX 19890101 MSH
EFFECTIVE_TIME 20060131 SNOMEDCT_US
HAS_GARD_PAGE true GARD
HN 89 MSH
IAN DEFAULT ICD10
IDENTIFIER_TYPE_ID 1 GARD
INCLUSION_TERM Allergic granulomatous angiitis ICD10
IS_ACTIVE true GARD
IS_RARE true GARD
IS_SPANISH false GARD
LAST_REVIEW_ACTION Synonym Added GARD
LAST_REVIEW_DATE 2009-12-15T00:00:00 GARD
MDA 19880518 MSH
MESH_DEFINITION Widespread necrotizing angiitis with granulomas. Pulmonary involvement is frequent. Asthma or other respiratory infection may precede evidence of vasculitis. Eosinophilia and lung involvement differentiate this disease from POLYARTERITIS NODOSA. NDFRT
MESH_DUI D015267 NDFRT
MESH_NAME Churg-Strauss Syndrome NDFRT
MESH_UI M0023506 NDFRT
MMR 20130708 MSH
MN C14.907.940.897.249.249 MSH
MN C15.604.515.292.015 MSH
MN C20.111.193.500 MSH
MODIFIER_ID 900000000000451002 SNOMEDCT_US
NDFRT_KIND DISEASE_KIND NDFRT
NUI N0000003214 NDFRT
ORDER_NO 17927 ICD10CM
PM 89 MSH
PRIMARY_PATH 10078117$10047112$10027665$10021428$Eosinophilic granulomatosis with polyangiitis$Vasculitides$Immune disorders NEC$Immune system disorders MDR
PRIMARY_SOC 10021428 MDR
PT_IN_VERSION 10.0 MDR
PT_IN_VERSION 10.1 MDR
PT_IN_VERSION 11.0 MDR
PT_IN_VERSION 11.1 MDR
PT_IN_VERSION 12.0 MDR
PT_IN_VERSION 12.1 MDR
PT_IN_VERSION 13.0 MDR
PT_IN_VERSION 13.1 MDR
PT_IN_VERSION 14.0 MDR
PT_IN_VERSION 14.1 MDR
PT_IN_VERSION 15.0 MDR
PT_IN_VERSION 15.1 MDR
PT_IN_VERSION 16.0 MDR
PT_IN_VERSION 16.1 MDR
PT_IN_VERSION 17.0 MDR
PT_IN_VERSION 17.1 MDR
PT_IN_VERSION 18.0 MDR
PT_IN_VERSION 18.1 MDR
PT_IN_VERSION 19.0 MDR
PT_IN_VERSION 19.1 MDR
PT_IN_VERSION 20.0 MDR
PT_IN_VERSION 20.1 MDR
PT_IN_VERSION 8.0 MDR
PT_IN_VERSION 8.1 MDR
PT_IN_VERSION 9.0 MDR
PT_IN_VERSION 9.1 MDR
RARE_DISEASE_URL http://rarediseases.info.nih.gov/gard/5776/allergic-angiitis/resources/1 GARD
RARE_DISEASE_URL http://rarediseases.info.nih.gov/gard/6111/churg-strauss-syndrome/resources/1 GARD
RXAUI 3107705 RXNORM
RXAUI 3107723 RXNORM
RXAUI 3109124 RXNORM
RXAUI 3133488 RXNORM
RXAUI 3133489 RXNORM
RXAUI 3254850 RXNORM
RXAUI 5930161 RXNORM
RXAUI 5930162 RXNORM
RXAUI 5930163 RXNORM
RXAUI 5930826 RXNORM
RXAUI 5931052 RXNORM
RXCUI 1023067 RXNORM
SMQ_TERM_ADDVERSION 12.0 MDR
SMQ_TERM_ADDVERSION 16.0 MDR
SMQ_TERM_ADDVERSION 19.1 MDR
SMQ_TERM_ADDVERSION 9.0 MDR
SMQ_TERM_CAT A MDR
SMQ_TERM_LEVEL 4 MDR
SMQ_TERM_LEVEL 5 MDR
SMQ_TERM_LMVERSION 12.0 MDR
SMQ_TERM_LMVERSION 16.0 MDR
SMQ_TERM_LMVERSION 19.1 MDR
SMQ_TERM_LMVERSION 9.0 MDR
SMQ_TERM_SCOPE 2 MDR
SMQ_TERM_STATUS A MDR
SMQ_TERM_WEIGHT 0 MDR
SNOMED_CID 82275008 NDFRT
SUBSET_MEMBER 447562003~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPADVICE~ALWAYS M30.1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPRULE~TRUE SNOMEDCT_US
SUBSET_MEMBER 447562003~MAPTARGET~M30.1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~CORRELATIONID~447561005 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~ALWAYS M30.1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPADVICE~IF GRANULOMATOUS ANGIITIS OF CENTRAL NERVOUS SYSTEM CHOOSE I67.7 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447637006 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPCATEGORYID~447639009 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPGROUP~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~1 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPPRIORITY~2 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~IFA 230734005 | Granulomatous angiitis of central nervous system | SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPRULE~OTHERWISE TRUE SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~I67.7 SNOMEDCT_US
SUBSET_MEMBER 6011000124106~MAPTARGET~M30.1 SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~X705i SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000508004~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000548007 SNOMEDCT_US
SUBSET_MEMBER 900000000000509007~ACCEPTABILITYID~900000000000549004 SNOMEDCT_US
TERMUI T044850 MSH
TERMUI T044851 MSH
TERMUI T044852 MSH
TERMUI T044853 MSH
TERMUI T044854 MSH
TERMUI T834097 MSH
TERMUI T834098 MSH
TERMUI T834099 MSH
TERMUI T834100 MSH
TERMUI T834101 MSH
TH NLM (1989) MSH
TH NLM (2014) MSH
TH ORD (2010) MSH
TH UNK (19XX) MSH
TYPE_ID 900000000000003001 SNOMEDCT_US
TYPE_ID 900000000000013009 SNOMEDCT_US

Additional Concept Data:  (none)

URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0008728

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