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Prolymphocytic Leukemia (CUI C0023486) Suggest changes to this concept
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Terms & Properties

Concept Unique Identifier (CUI): C0023486

NCI Thesaurus Code: C3181  (see NCI Thesaurus info)

Semantic Type: Neoplastic Process

NCIt Definition: A mature B- or T- cell leukemia with progressive clinical course. It is characterized by the presence of medium-sized lymphocytes with visible nucleoli (prolymphocytes) in the peripheral blood, bone marrow, and spleen.

PDQ Definition: A mature B- or T- cell leukemia with progressive clinical course. It is characterized by the presence of medium-sized lymphocytes with visible nucleoli (prolymphocytes) in the peripheral blood, bone marrow, and spleen. (NCI Thesaurus)

NCI-GLOSS Definition: A type of chronic lymphocytic leukemia (CLL) in which too many immature white blood cells (prolymphocytes) are found in the blood and bone marrow. PLL usually progresses more rapidly than classic CLL.

CTEP Definition: CTEP_For_FDA: 10036888/Prolymphocytic leukemia

MSH Definition: A chronic leukemia characterized by a large number of circulating prolymphocytes. It can arise spontaneously or as a consequence of transformation of CHRONIC LYMPHOCYTIC LEUKEMIA.

Synonyms & Abbreviations: (see Synonym Details)
Leukemia, Prolymphocytic
Leukemias, Prolymphocytic
PLL - Prolymphocytic leukaemia
PLL - Prolymphocytic leukemia
PLL
Pro-lymphocytic leukaemia
Pro-lymphocytic leukemia
Prolymphocytic leukaemia (clinical)
Prolymphocytic leukaemia
Prolymphocytic leukemia (B or T)
Prolymphocytic leukemia (B or T-cell)
Prolymphocytic leukemia (clinical)
Prolymphocytic leukemia (disorder)
Prolymphocytic leukemia (morphologic abnormality)
Prolymphocytic leukemia, NOS
Prolymphocytic Leukemias
Prolymphocytic Leukemia

External Source Codes: 
NCI Thesaurus Code C3181 (see NCI Thesaurus info)

Other Properties: Property Definitions
Name Value Source
ACTIVE 1 SNOMEDCT_US
AQL BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI MSH
CASE_SIGNIFICANCE_ID 900000000000017005 SNOMEDCT_US
CASE_SIGNIFICANCE_ID 900000000000448009 SNOMEDCT_US
Contributing_Source CTEP NCI
Contributing_Source CTRP NCI
Contributing_Source GDC NCI
CTV3ID B64y1 SNOMEDCT_US
CTV3ID BBr25 SNOMEDCT_US
DC 1 MSH
DEFINITION_STATUS_ID 900000000000073002 SNOMEDCT_US
DEFINITION_STATUS_ID 900000000000074008 SNOMEDCT_US
DX 19890101 MSH
EFFECTIVE_TIME 20020131 SNOMEDCT_US
HN 89 MSH
ICD-O-3_CODE 9832/3 SNOMEDCT_US
ICD-O-3_Code 9832/3 NCI
MDA 19880609 MSH
MMR 20230531 MSH
MN C04.557.337.428.565 MSH
MN C15.378.508.428.565 MSH
MN C15.604.515.560.550 MSH
MN C20.683.515.528.565 MSH
NCI_THESAURUS_CODE C3181 PDQ
Neoplastic_Status Malignant NCI
ORIG_STY Neoplasm diagnosis PDQ
PID 4780 PDQ
PM 89 MSH
PRIMARY_PATH 10036888$10024295$10024324$10029104$Prolymphocytic leukaemia$Leukaemias chronic lymphocytic$Leukaemias$Neoplasms benign, malignant and unspecified (incl cysts and polyps) MDR
PRIMARY_SOC 10029104 MDR
PT_IN_VERSION 10.0 MDR
PT_IN_VERSION 10.1 MDR
PT_IN_VERSION 11.0 MDR
PT_IN_VERSION 11.1 MDR
PT_IN_VERSION 12.0 MDR
PT_IN_VERSION 12.1 MDR
PT_IN_VERSION 13.0 MDR
PT_IN_VERSION 13.1 MDR
PT_IN_VERSION 14.0 MDR
PT_IN_VERSION 14.1 MDR
PT_IN_VERSION 15.0 MDR
PT_IN_VERSION 15.1 MDR
PT_IN_VERSION 16.0 MDR
PT_IN_VERSION 16.1 MDR
PT_IN_VERSION 17.0 MDR
PT_IN_VERSION 17.1 MDR
PT_IN_VERSION 18.0 MDR
PT_IN_VERSION 18.1 MDR
PT_IN_VERSION 19.0 MDR
PT_IN_VERSION 19.1 MDR
PT_IN_VERSION 20.0 MDR
PT_IN_VERSION 20.1 MDR
PT_IN_VERSION 21.0 MDR
PT_IN_VERSION 21.1 MDR
PT_IN_VERSION 22.0 MDR
PT_IN_VERSION 22.1 MDR
PT_IN_VERSION 23.0 MDR
PT_IN_VERSION 23.1 MDR
PT_IN_VERSION 24.0 MDR
PT_IN_VERSION 24.1 MDR
PT_IN_VERSION 25.0 MDR
PT_IN_VERSION 25.1 MDR
PT_IN_VERSION 26.0 MDR
PT_IN_VERSION 8.0 MDR
PT_IN_VERSION 8.1 MDR
PT_IN_VERSION 9.0 MDR
PT_IN_VERSION 9.1 MDR
SMQ_TERM_ADDVERSION 10.0 MDR
SMQ_TERM_CAT A MDR
SMQ_TERM_LEVEL 4 MDR
SMQ_TERM_LEVEL 5 MDR
SMQ_TERM_LMVERSION 20.0 MDR
SMQ_TERM_SCOPE 2 MDR
SMQ_TERM_STATUS A MDR
SMQ_TERM_WEIGHT 0 MDR
SUBSET_MEMBER 446608001~MAPTARGET~9832/3 SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~B64y1 SNOMEDCT_US
SUBSET_MEMBER 900000000000497000~MAPTARGET~BBr25 SNOMEDCT_US
TERM_LEVEL Preferred ICDO
TERMUI T045737 MSH
TERMUI T045738 MSH
TH NLM (1989) MSH
TH UNK (19XX) MSH
TYPE_ID 900000000000003001 SNOMEDCT_US
TYPE_ID 900000000000013009 SNOMEDCT_US

Additional Concept Data:  (none)

URL to Bookmark: https://ncim-stage.nci.nih.gov/ncimbrowser/ConceptReport.jsp?dictionary=NCI Metathesaurus&code=C0023486

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